Short communicationIctal SPECT in Sturge-Weber syndrome
Section snippets
Case report
A 6-year-old boy had frequent daily bilateral asymmetric tonic seizures since he was 8 months old. He had been diagnosed to have right-sided SWS. He had flaccid hemiparesis on left side more than on the right, and was not able to stand or walk. He was mentally retarded and unable to speak. As he was resistant to multiple anti-epileptic drugs (AED), epilepsy surgery was performed in 2003. Temporal and central lobectomy and frontal and occipital hemispherotomy were performed on the right side. He
Discussion
Our patient demonstrates that even if previous epilepsy surgery, for example, combined hemispherectomy and hemispherotomy has failed in SWS patients, they may benefit from repeated surgery if the seizure onset zone can be localized. Epilepsy surgery should be considered in these patients if high seizure frequency and developmental deterioration do not respond to AED treatment. Anatomical hemispherectomy has an excellent outcome but was formerly reported to be associated with chronic
Conflicts of interest statement
The authors report no conflicts of interest.
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